Journal of Oral Health and Community Dentistry

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VOLUME 1 , ISSUE 2 ( May-August, 2007 ) > List of Articles


Xeroderma Pigmentosa; Review and Case Report

CM Marya, Rajesh Anegundi

Citation Information : Marya C, Anegundi R. Xeroderma Pigmentosa; Review and Case Report. J Oral Health Comm Dent 2007; 1 (2):43-45.

DOI: 10.5005/johcd-1-2-43

License: CC BY-NC 3.0

Published Online: 01-09-2012

Copyright Statement:  Copyright © 2007; The Author(s).


Xeroderma Pigmentosa is caused by an autosomal recessive allele. It is characterized by dry, pigmented skin, spidery blood vessels in the skin, skin cancers, and sometimes other abnormalities of both the eyes and brain. A harsh reaction to sunlight, such as severe sunburn and blistering at only a slight exposure, is a notable symptom and should be distinguished within the first year or two of life. The majority of the people who are born with these disorders die by early adulthood due to malignant cancers. This article reports a case of 6-year-old child suffering from XP with dental implications.

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